How I treat hemophagocytic lymphohistiocytosis
نویسندگان
چکیده
منابع مشابه
How I treat hemophagocytic lymphohistiocytosis.
Hemophagocytic lymphohistiocytosis (HLH) is a syndrome of pathologic immune activation, occurring as either a familial disorder or a sporadic condition, in association with a variety of triggers. This immune dysregulatory disorder is prominently associated with cytopenias and a unique combination of clinical signs and symptoms of extreme inflammation. Prompt initiation of immunochemotherapy is ...
متن کاملHow I treat How I treat hemophagocytic lymphohistiocytosis
Hemophagocytic lymphohistiocytosis (HLH) is a syndrome of pathologic immune activation, occurring as either a familial disorder or a sporadic condition, in association with a variety of triggers. This immune dysregulatory disorder is prominently associated with cytopenias and a unique combination of clinical signs and symptoms of extreme inflammation. Prompt initiation of immunochemotherapy is ...
متن کاملHow I treat hemophagocytic lymphohistiocytosis in the adult patient.
Hemophagocytic lymphohistiocytosis (HLH) is a devastating disorder of uncontrolled immune activation characterized by clinical and laboratory evidence of extreme inflammation. This syndrome can be caused by genetic mutations affecting cytotoxic function (familial HLH) or be secondary to infectious, rheumatologic, malignant, or metabolic conditions (acquired HLH). Prompt recognition is paramount...
متن کاملHow I Treat Hemophagocytic Lymphohistiocytosis in the Adult Patient Alison
Hemophagocytic Lymphohistiocytosis (HLH) is a devastating disorder of uncontrolled immune activation characterized by clinical and laboratory evidence of extreme inflammation. This syndrome can be caused by genetic mutations affecting cytotoxic function (familial HLH) or secondary to infectious, rheumatologic, malignant, or metabolic conditions (acquired HLH). Prompt recognition is paramount an...
متن کاملHow I Treat How I treat hemophagocytic lymphohistiocytosis in the adult patient
Hemophagocytic lymphohistiocytosis (HLH) is a rare and devastating disorder of uncontrolled immune activation that has gained increasing recognition over the past decade. Patients with HLH present with clinical and laboratory evidence of extreme inflammation. This syndrome was first described in 1939 by Scott and Robb-Smith and again in 1952 when Farquhar and Claireaux reported a case of 2 infa...
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ژورنال
عنوان ژورنال: Blood
سال: 2011
ISSN: 0006-4971,1528-0020
DOI: 10.1182/blood-2011-03-278127